Scientific Articles
Aug 15, 2017
Amyloidosis is a condition characterized by the extracellular deposition of amyloid, a fibrillary substance consisting of low-molecular-weight protein subunits.…
Jul 12, 2017
The amyloidoses are a group of systemic diseases characterized by organ deposition of misfolded protein fragments of diverse origins. The natural history of the…
Jun 13, 2017
Laryngotracheal amyloid deposition is an uncommon manifestation of systemic light chain amyloidosis. Diagnostic imaging, such as CT, is useful for suggesting the…
Jun 12, 2017
Hereditary transthyretin-mediated (hATTR) amyloidosis is a progressive disease characterized by deposition of amyloid fibrils in various organs and tissues of the…
Apr 12, 2017
Cardiac amyloidosis occurs because of abnormal protein (amyloid) deposition in the cardiac tissue. Even with advanced diagnostic techniques and treatments, the…
Apr 10, 2017
Introduction:
A systematic literature review on systemic light chain (AL) amyloidosis was conducted in order to understand the disease burden, and identify unmet…
Mar 21, 2017
The role of older generations in families with hereditary diseases has been recognised and associated to their function as guardians of the family's medical history…
Dec 25, 2016
Systemic light-chain (AL) amyloidosis is an infiltrative disorder associated with an underlying plasma cells dyscrasia, in which monoclonal immunoglobulin light…
Nov 28, 2016
Systemic amyloidoses are rare and proteiform diseases, caused by extracellular accumulation of insoluble misfolded fibrillar proteins. Prognosis is dictated by…
Nov 16, 2016
Cardiac amyloidosis is an underrecognized condition, in which delays to diagnosis have great implications on management options, prognosis, and morbidity. Once…